ELISA CLN5 anti-

Quantity :100µL Clone Number: Aliases:Ceroid lipofuscinosis neuronal 5 antibody; Ceroid-lipofuscinosis neuronal protein 5 antibody; CLN5 antibody; CLN5_ antibody; NCL antibody; Protein CLN5 antibody Product Type:Polyclonal Antibody Immunogen Species:Homo sapiens () UniProt ID:O75503 Immunogen:SyntheQuantityd peptide derived from internal of CLN5. Raised in:Rabbit Reactivity: Tested Applications:ELISA, WB; WB:1:500-1:3000 Background:This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thoµght to be associated with lysosomal storage function. Savukoski M., Nat. Genet. 19:286-288(1998). Dunham A., Nature 428:522-528(2004). Clonality:Polyclonal Isotype:IgG Purification Method:The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. Conjµgate:Non-conjµgated Buffer:Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. Form:liquid Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Target Names:CLN5 Research Areas:Neuroscience